Arylsulfatase B encoded by this gene belongs to the sulfatase family. The arylsulfatase B homodimer hydrolyzes sulfate groups of N-Acetyl-D-galactosamine, chondriotin sulfate, and dermatan sulfate. The protein is targetted to the lysozyme. Defects in this gene cause Maroteaux-Lamy syndrome. Two alternatively spliced transcript variants encoding distinct isoforms have been found for this gene.
